中国麻风皮肤病杂志 ›› 2022, Vol. 38 ›› Issue (10): 734-735.doi: 10.12144/zgmfskin202210734

• 病例报告 • 上一篇    下一篇

节段型皮肤僵硬综合征一例

陈佳林,陈声利,卢宪梅,施仲香   

  1. 山东第一医科大学附属皮肤病医院(山东省皮肤病医院),山东省皮肤病性病防治研究所,济南,250022
  • 出版日期:2022-10-15 发布日期:2022-08-23

Segmental stiff skin syndrome: a case report

CHEN Jialin, CHEN Shengli, LU Xianmei, SHI Zhongxiang   

  1. Shandong Provincial Hospital for Skin Diseases & Shandong Provincial Institute of Dermatology and Venereology, Shandong First Medical University, Jinan 250022,China
  • Online:2022-10-15 Published:2022-08-23

摘要: 我们报道一例节段型皮肤僵硬综合征。患者,男,14岁。腹部皮肤硬化6年。病理活检示:真皮深层胶原纤维增生,成纤维细胞增多,散在的脂肪细胞灶,浅筋膜胶原纤维粗大,阿新蓝染色阴性。

Abstract: We report a case of segmental stiff skin syndrome. A 14-year-old man attended our clinic with a 6-year history of the skin induration on his abdomen. Histological examination  revealed broadened and elongated collagen fibrils in deep dermis, increased fibrocytes, clusters of lipocytes, thickening collagen fibrils in superficial fascia, alcian blue staining was negative.