Abstract: Tuberous sclerosis complex (TSC) is an autosomal dominant hereditary disease involving multiple systems. We report a 20-year-old male patient with a 9-year history of multiple facial papules. Dermatological examination showed scattered or clustered round, firm and smooth-surfaced papules on both cheeks, nose and perioral area, eight scattered hypopigmented macules of different sizes on the neck, trunk and buttocks, a slightly elevated light brown plaque of 10 cm × 13 cm on the left shoulder, and pitted enamel defects on the teeth. Cranial CT revealed nodular high-density lesions in the right cerebellum, beside the bodies of bilateral lateral ventricles and the internal capsule, while abdominal CT presented multiple nodular and patchy low-density lesions in both kidneys suggestive of hamartomas. Diagnosis: Tuberous sclerosis. Over ten red papules on the face were treated with one laser session, after which they fell off,subsequent follow-up was lost.

Key words: tuberous selerosis complex, renal angiomyolipoma