中国麻风皮肤病杂志 ›› 2021, Vol. 37 ›› Issue (4): 233-235.doi: 10.12144/zgmfskin202104233

• 病例报告 • 上一篇    下一篇

节段性皮肤僵硬综合征一例

王锋1,张亚芹1,孟祥羽1,杨加琳2,蒋宏博3   

  1. 1吉林大学第二医院皮肤科，吉林长春，130000；
    2西安医学院第一附属医院皮肤科，陕西西安，710000；
    3青岛市妇女儿童医院皮肤科，山东青岛，266000
  • 出版日期:2021-04-15 发布日期:2021-04-07
  • 通讯作者: 张亚芹，E-mail: zyqjdey@163.com

Segmental stiff skin syndrome: a case report

WANG Feng1, ZHANG Yaqin1, MENG Xiangyu1, YANG Jialin2, JIANG Hongbo3   

  1. 1 Department of Dermatology, The Second Hospital of Jilin University, Changchun 130000, China; 
    2 Department of Dermatology, The First Hospital of Xi'an Medical University, Xi'an 710000, China;
    3 Department of Dermatology, Qingdao Women's and children's Hospital, Qingdao 266000, China.
  • Online:2021-04-15 Published:2021-04-07
  • Contact: ZHANG Yaqin, E-mail: zyqjdey@163.com

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摘要： 患儿，男，8岁。因右侧股部、臀部及腰部皮肤触之僵硬8年就诊。患者皮损呈单侧分布，伴有轻度多毛和色素沉着。病理活检示表皮过度角化，基底层色素增加，真皮中层胶原纤维增粗、致密,呈均质化，无炎症细胞浸润，附属器未见异常。阿新蓝染色呈阳性。综上诊断为节段性皮肤僵硬综合征。

关键词: 节段性皮肤僵硬综合征, 线状硬皮病

Abstract: A 8-year-old boy was seen for indurated skin of right thigh, buttock and waist for 8 years. The lesions were unilateral with mild hypertrichosis and pigmentation. Skin histology showed hyperkeratosis of the epidermis, increased pigment in the basal layer, and thickened dense collagen fibers in the middle dermis with no obvious inflammatory infiltrates and no obvious atrophy of appendages. Alcian blue stainingwas positive. The diagnosis of segmental stiff skin syndrome was made. 

Key words: segmental stiff skin syndrome, linear scleroderma