Abstract: Relapsing linear acantholytic dermatosis is a rare disease. We report a case of relapsing linear acantholytic dermatosis. A six-year-old girl presented with recurrent erythematous and plaque on the right hip and posterior thigh for 5 years, with aggravation for 2 months. Linear erythematous plaques with overlying white scale and localized bloody scrab was on her right hip, right posterior thigh and popliteal fossa, and pigmentation scattered was seen. The lesion distributed along with the Blaschko line. Histopathological examination showed hyperkeratosis as well as parakeratosis, acantholysis like a collapsed wall. Direct immunofluorescence (DIF) showed negative result.

Key words: relapsing, linear acantholysis, Blaschko line