中国麻风皮肤病杂志 ›› 2022, Vol. 38 ›› Issue (3): 174-175.doi: 10.12144/zgmfskin202203174

• 病例报告 • 上一篇    下一篇

节段性皮肤僵硬综合征一例

陈声利,卢宪梅,刘红,陈学超   

  1. 山东第一医科大学附属皮肤病医院(山东省皮肤病医院),山东省皮肤病性病防治研究所,济南,250022
  • 出版日期:2022-03-15 发布日期:2022-01-05
  • 通讯作者: 陈声利,E-mail: shengli28@163.com

A case of segmental stiff skin syndrome

CHEN Shengli, LU Xiangmei, LIU Hong, CHEN Xuechao   

  1. Shandong Provincial Hospital for Skin Diseases & Shandong Provincial Institute of Dermatology and Venereology, Shandong First Medical University & Shandong Academy of Medical Sciences, Jinan 250022, China
  • Online:2022-03-15 Published:2022-01-05
  • Contact: CHEN Shengli, E-mail: shengli28@163.com

摘要: 患儿,男,5岁。左股部皮肤硬化、多毛4年余。皮损组织病理示:真皮胶原纤维增多、增粗,排列紊乱,缺乏炎症,胶原纤维间可见脂肪细胞。阿新蓝染色:真皮内黏蛋白增多。诊断:皮肤僵硬综合征。

关键词: 皮肤僵硬综合征, 临床特征, 组织病理

Abstract: A 5-year-old boy presented with stiff skin and hypertrichosis on the left thigh for four years. Histological examination showed thickening and proliferating bundles of haphazardly arranged collagen fibers without infiltration of inflammatory cells. Adipose tissue was present between the collagen fibers. Staining of Alcian blue showed dermal deposits of mucin. The diagnosis of segmental stiff skin syndrome was made.

Key words: stiff skin syndrome, clinical features, histopathologic features