Abstract: A fifteen-year-old boy presented with linear and whorled hyperpigmentation all over his body for fifteen years. There was a local protrusion on his left buttock at birth. He was found limping when he was a toddler. X-ray imaging showed that the right lower limb was shorter than another. The diagnosis of linear and whorled nevoid hypermelanosis with skeletal abnormality was made.

Key words: ypermelanosis')">

ypermelanosis, linear, whorled, skeletal abnormality