Abstract: Clinically amyopathic dermatomyositis is a rare subtype of dermatomyositis, which presents with cutaneous lesions of classic dermatomyositis but lacks characteristic myopathy. Compared with its classic dermatomyositis, clinically amyopathic dermatomyositis has distinctive myositis specific auto-antibodies and different prognostic features in terms of interstitial lung disease and malignancy, which are reviewed in this paper.

Key words: dermatomyositis, clinically amyopathic dermatomyositis, interstitial lung disease, malignancy