中国麻风皮肤病杂志 ›› 2023, Vol. 39 ›› Issue (10): 737-740.doi: 10.12144/zgmfskin202310737

• 病例报告 • 上一篇    下一篇

伴多发性骨髓瘤的原发性系统性淀粉样变一例

成春梅1,徐静2,马琼1,倪昌雯2   

  1. 1大理大学临床医学院,云南大理, 671000;2大理大学第一附属医院皮肤科,云南大理,671000
  • 出版日期:2023-10-15 发布日期:2023-10-11

Primary systemic amyloidosis with multiple myeloma: a case report

CHENG  Chunmei1, XU Jing2, MA Qiong1, NI Changwen2   

  1. 1 Clinical Medical College, Dali University, Dali 671000, China; 2 Department of Pathology, First Affiliated Hospital of Dali University, Dali 671000, China
  • Online:2023-10-15 Published:2023-10-11

摘要: 原发性系统性淀粉样变是一种罕见的单克隆浆细胞病,早期症状缺乏特异性,临床容易误诊。本文报道一例以皮肤紫癜、甲受损、充血性心力衰竭为主要特征的伴多发性骨髓瘤的原发性系统性淀粉样变的临床病例。

关键词: 免疫球蛋白轻链型淀粉样变, 系统性淀粉样变, 多发性骨髓瘤, 紫癜

Abstract: Primary systemic amyloidosis is a disease of rare monoclonal plasma cell, the early symptoms lack specificity and clinically easily misdiagnosed. We report a clinical case of primary systemic amyloidosis with multiple myeloma characterized by purpura, nail damage, and congestive heart failure.

Key words: immunoglobulin light chain amyloidosis, systemic amyloidosis, multiple myeloma, purpura