中国麻风皮肤病杂志 ›› 2022, Vol. 38 ›› Issue (12): 908-911.doi: 10.12144/zgmfskin202212908

• 综述 • 上一篇    下一篇

临床无肌病性皮肌炎预后相关特征研究进展

李毓芬,姜祎群   

  1. 中国医学科学院北京协和医学院皮肤病医院病理科，南京，210042
  • 出版日期:2022-12-15 发布日期:2022-10-27

Research progress on prognostic features of clinically amyopathic dermatomyositis

LI Yufen, JIANG Yiqun   

  1. Department of Dermatopathology, Hospital for Skin Diseases, Inslitute of Dermatology, Chinese Academy of Medical Sciences and Peking Union Medical College, Nanjing 210042, China
  • Online:2022-12-15 Published:2022-10-27

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摘要： 临床无肌病性皮肌炎是皮肌炎的特殊亚型，表现为典型皮肌炎的皮肤病变，但缺乏特征性肌病。与经典皮肌炎相比，临床无肌病性皮肌炎在肌炎特异性自身抗体谱和间质性肺病、恶性肿瘤方面具有其独特预后特征，本文对其进行综述。

关键词: 皮肌炎, 临床无肌病性皮肌炎, 间质性肺病, 恶性肿瘤

Abstract: Clinically amyopathic dermatomyositis is a rare subtype of dermatomyositis, which presents with cutaneous lesions of classic dermatomyositis but lacks characteristic myopathy. Compared with its classic dermatomyositis, clinically amyopathic dermatomyositis has distinctive myositis specific auto-antibodies and different prognostic features in terms of interstitial lung disease and malignancy, which are reviewed in this paper.

Key words: dermatomyositis, clinically amyopathic dermatomyositis, interstitial lung disease, malignancy