中国麻风皮肤病杂志 ›› 2023, Vol. 39 ›› Issue (8): 606-608.doi: 10.12144/zgmfskin202308606

• 病例报告 • 上一篇    下一篇

表现为红皮病的大疱性类天疱疮伴天疱疮抗体阳性一例

张坤,陈丽秀   

  1. 重庆市开州区人民医院,重庆,405400
  • 出版日期:2023-08-15 发布日期:2023-07-19

Bullous pemphigoid with positive pemphigus antibody in erythroderma: a case report

ZHANG Kun, CHEN Lixiu   

  1. Chongqing Kaizhou District People's Hospital, Chongqing  405400, China
  • Online:2023-08-15 Published:2023-07-19

摘要: 红皮病又称剥脱性皮炎,是一种以全身 90%以上皮肤潮红、脱屑为特征的炎症性疾病。大疱性类天疱和寻常型天疱疮是两类截然不同的自身免疫性水疱病。现报道1例以红皮病收住入院,完善相关检查后诊断为大疱性类天疱疮伴天疱疮抗体阳性的患者。给予足量、足疗程系统使用糖皮质激素联合免疫抑制剂及静脉输注人免疫球蛋白治疗后控制病情。

关键词: 红皮病, 大疱性类天疱, 天疱疮抗体, 治疗

Abstract: Erythroderma, also known as exfoliative dermatitis, is an inflammatory disease characterized by flushing and desquamation of more than 90% of the skin. Bullous pemphigoid and pemphigus vulgaris are two different types of autoimmune blister diseases. It is reported that a case of erythroderma who was diagnosed as bullous pemphigoid with positive pemphigus antibody after finishing the auxiliary examination. The disease was controlled after adequate and full course of systematic use of corticosteroids combined with immunosuppressants and intravenous infusion of human immunoglobulin.

Key words: erythroderma, bullous pemphigoid, positive pemphigus antibody, treatment