Abstract: Type C lymphomatoid papulosis is rare, herein we report a case in this paper. A 13-year-old boy presented with recurrent red papular nodules all over the body for 2 years, with partial nodules breaking down in the central. Physical examination showed no abnormalities, and he was early diagnosed as pityriasis lichenoides et varioliformis acuta. Histopathological biopsy showed diffuse infiltration of large anaplastic lymphocytes with consistent morphology in the dermis and subcutaneous tissue of the tumor. Immunohistochemical showed CD2 (+++), CD8 (+), CD30 (+++), GranzymeB (+), Ki67 (+ 90%), TI-A(+) , test positive for TCR gene rearrangement. The dignosis of type C lymphomatoid papulosis was finally made.

Key words: lymphomatoid papulosis, children, immunohistochemistry